Title: Impact of Growth Friendly Interventions on Spine and Pulmonary Outcomes of Patients with Spinal Muscular Atrophy Publication Summary
Authors: Ishaan Swarup, Elle M. MacAlpine, Oscar H. Mayer, Robert K. Lark, John T. Smith, Michael G. Vitale, John M. Flynn, Jason B. Anari, Pediatric Spine Study Group, Patrick J. Cahill
Journal: European Spine Journal
Date: August 01, 2020
Excerpt:
Patients with spinal muscular atrophy (SMA) are often treated with growth-friendly devices such as vertical expandable prosthetic titanium rib (VEPTR) and magnetically controlled growing rods(MCGR) to correct spinal deformity and improve pulmonary function. There is limited data on this topic, and the purpose of this study was to assess the effect of these constructs and the addition of chest wall support (CWS) on spinal deformity, chest structure and pulmonary outcomes.
Keywords: Spinal muscular atrophy, Early-onset scoliosis, Thoracic insufficiency syndrome, Vertical expandable prosthetic titanium rib, Growing rod